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Answer» What is Klippel-Trenaunay syndrome mean? Klippel–Trénaunay syndrome, formerly Klippel–Trénaunay–Weber syndrome and sometimes angioosteohypertrophy syndrome and hemangiectatic hypertrophy, is a rare congenital medical condition in which blood vessels and/or lymph vessels fail to form properly. The three main features are nevus flammeus (port-wine stain), venous and lymphatic malformations, and soft-tissue hypertrophy of the affected limb. It is similar to, though distinctly separate from, the less common Parkes Weber syndrome. The classical triad of Klippel–Trenaunay syndrome consists of: vascular malformations of the capillary, venous and lymphatic vessels;varicosities of unusual distribution, particularly the lateral venous anomaly; andunilateral soft and skeletal tissue hypertrophy, usually the lower extremity. reference
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